Prophylaxis in Hemophilia

نویسندگان

چکیده

Hemophilia is an inherited X-linked coagulopathy defined by a deficiency or abnormality in the clotting function of factor VIII (Hemophilia A) IX B). Prophylaxis – regular administration therapeutic products to maintain hemostasis and prevent bleeding mainstream treatment. Addressing development scientific evidence for administrating prophylaxis goal this review. modality choice people with severe hemophilia, being considered, principle, lifelong It should have early onset, ideally as primary, at least secondary. Even tertiary seems offer benefit, although further studies are still lacking. Individualized strategies lead optimization dilemma between better joint outcomes versus involved costs.

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ژورنال

عنوان ژورنال: Clinical & Biomedical Research

سال: 2023

ISSN: ['2357-9730']

DOI: https://doi.org/10.22491/2357-9730.126436